Demencia de rápida progresión y mioclonías
- Villamil-Cajoto, Iago
- González-Quintela, A.
- Villacian-Vicedo, María José
ISSN: 0304-4858, 2173-2302
Year of publication: 2005
Volume: 102
Issue: 4
Pages: 71-74
Type: Article
More publications in: Gaceta médica de Bilbao: Revista oficial de la Academia de Ciencias Médicas de Bilbao. Información para profesionales sanitarios
Abstract
Cognoscitive deterioration processes are quite common in the usual pathology managed incertain Services. Main causes are related with degenerative dementia. In those cases of rapidprogressive evolution, other processes, should be excluded. We present one patient admittedbecause of cognitive deficit. Myoclonus wereobserved during admission andelectroencephalogram showed characteristic complexes compatible among others withCreuzfeldt-Jakob disease. Protein 14-3-3 study was developed and turned positive. Accordingto World Health Organization and European Surveillance Group classification criteria forspongiform encephalopaties, this case fulfilled “probable” criteria. Clinical evolution with morethan 2 years of survival after diagnosis did not confirm diagnosis. We made a review ofdiagnostic tests and false positive cases such as: vascular cerebral disease, viral encepahlitis,glioblastoma, cerebral metastasis and hipoxemic cerebral damage.