Síndrome de Gorlin (Síndrome Nevoide Basocelular)
- B. De-Domingo
- F. González
- P. Lorenzo
ISSN: 0365-6691
Year of publication: 2008
Volume: 83
Issue: 5
Pages: 321-324
Type: Article
More publications in: Archivos de la Sociedad Española de Oftalmologia
Abstract
Clinical case: A 77 year-old male patient with Parkinsons disease and senile dementia had many facial basal cell carcinomas and an ectropion of the left eye. When he experienced respiratory difficulty he was diagnosed to have an ameloblastoma in left nostril requiring surgery. Discussion: Gorlin syndrome is an autosomal dominant condition characterized by basal cell carcinomas, and skeletal and neurological anomalies. The presence of multiple basal cell carcinomas on the eyelids in a child or in a young patient should alert ophthalmologists to the possibility of this syndrome.
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