Cuidados enfermeros en la extrofia vesical neonatal

  1. Fernández Tuñas, Mª del Carmen
  2. Turnes Paredes, Margarita
  3. Ces Tarrío, Mª del Carmen
  4. Couce Pico, María Luz
  5. Pérez Muñuzurri, Alejandro
Journal:
Metas de enfermería

ISSN: 1138-7262

Year of publication: 2014

Volume: 17

Issue: 9

Type: Article

More publications in: Metas de enfermería

Abstract

Vesical Exstrophy (VE) is a rare congenital alteration which consists in the protrusion of the bladder through the abdominal wall, and it requires a complex and fast surgical intervention, often by a multidisciplinary team. This is a rare disease, which appears in one out of 35,000-40,000 newborns, and it is more frequent in males. Even though its etiology is not very well defined, there seems to be a genetic predisposition. It occurs due to a defect of migration in the infraumbilical mesenchyma cells, which will lead to the formation of the lower abdominal wall, genital tubercles and pubic branches. The treatment for VE is surgical, and often in various stages. One of the problems in these patients is sphincter control, once they have undergone surgery. Children who undergo reconstructive surgery at the time of birth will achieve better results regarding urinary incontinence, which is one of the great problems. Nursing care before and after surgery is very important for the recovery of these patients, because they must remain immobile during several days in order to achieve an adequate bladder closure.

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